Ameloblastic Fibrossarcoma In The Mandible: A Case Report

Fibrossarcoma Ameloblástico na mandíbula: um relato de caso

Authors

DOI:

https://doi.org/10.17765/2176-9206.2025v18e12676

Keywords:

Odontogenic tumors, fibrosarcoma, malignant neoplasms, mandible, case report

Abstract

 

Ameloblastic fibrosarcoma is a rare malignant neoplasm, commonly found in the mandible and with higher prevalence in men. Extensive expansion and increased volume are the main clinical characteristics observed. Objective: To report a case of ameloblastic fibrosarcoma in a 73-year-old female patient, presenting with swelling in the chin area and deformity on the right side of the mandible. Methodology: To confirm the diagnosis, two incisional biopsies and radiographic examinations were performed. Results: The first histopathological examination showed proliferation of stroma and odontogenic epithelium with benign neoplasia, and negative immunohistochemical staining for Ki-67. The second examination revealed an ameloblastic appearance, confirming the diagnosis of ameloblastic fibrosarcoma. Treatment consisted solely of complete resection of the mandible. Conclusion: The rarity of this tumor underscores the importance of disseminating the clinical, radiographic, and histological findings of this case. Accurate diagnosis is crucial for early and conservative treatment, determining factors for patient cure and survival.

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Author Biographies

Christian Simões Ferreira, Faculty of Ilhéus

Dental surgeon from the Faculty of Ilhéus. Volunteer scientific initiation student. Has a line of research on actinic cheilitis. He completed an internship at Hospital de Amor (Barretos). He has experience in hospital dentistry and diagnosis. He currently works at UP Odontologia e Bem Estar in Porto Seguro (BA).

Thaynara Nany Bicalho do Carmo, Faculty of Ilhéus

Dental surgeon graduated from the Faculty of Ilhéus. Currently works in a private clinic in the city of Jequié (BA)

Rebeca Carolina Moraes Dantas, Faculty of Ilhéus

Graduated in Dentistry from the State University of Feira de Santana, UEFS, Specialist in Stomatology from the Brazilian Association of Dentistry - Bahia section, ABO-BA, Master in Dentistry from the Federal University of Pernambuco, UFPE and PhD in Dentistry and Health from the Federal University of Bahia , UFBA. Currently, she works as a Dental Surgeon at the Federal Institute of Education, Science and Technology Baiano-Campus Uruçuca, IFBAIANO and works in a private clinic in the areas of Stomatology and Laser Therapy.

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Published

2024-07-21

How to Cite

Ferreira, C. S., Carmo, T. N. B. do, & Dantas, R. C. M. (2024). Ameloblastic Fibrossarcoma In The Mandible: A Case Report: Fibrossarcoma Ameloblástico na mandíbula: um relato de caso. Saúde E Pesquisa, 18, e12676. https://doi.org/10.17765/2176-9206.2025v18e12676

Issue

Section

Relato de Casos