Ameloblastic Fibrossarcoma In The Mandible: A Case Report
Fibrossarcoma Ameloblástico na mandíbula: um relato de caso
DOI:
https://doi.org/10.17765/2176-9206.2025v18e12676Keywords:
Odontogenic tumors, fibrosarcoma, malignant neoplasms, mandible, case reportAbstract
Ameloblastic fibrosarcoma is a rare malignant neoplasm, commonly found in the mandible and with higher prevalence in men. Extensive expansion and increased volume are the main clinical characteristics observed. Objective: To report a case of ameloblastic fibrosarcoma in a 73-year-old female patient, presenting with swelling in the chin area and deformity on the right side of the mandible. Methodology: To confirm the diagnosis, two incisional biopsies and radiographic examinations were performed. Results: The first histopathological examination showed proliferation of stroma and odontogenic epithelium with benign neoplasia, and negative immunohistochemical staining for Ki-67. The second examination revealed an ameloblastic appearance, confirming the diagnosis of ameloblastic fibrosarcoma. Treatment consisted solely of complete resection of the mandible. Conclusion: The rarity of this tumor underscores the importance of disseminating the clinical, radiographic, and histological findings of this case. Accurate diagnosis is crucial for early and conservative treatment, determining factors for patient cure and survival.
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